Congenital duodenal obstruction (CDO) affects 1.2 out of every 10,000 live newborns and is usually accompanied with other abnormalities, the most common of which is cardiac. The goal of this study was to report significant results one year after surgical repair. The British Association of Paediatric Surgeons Congenital Anomaly Surveillance System was used in this prospective population-based investigation. During a 12-month period beginning in March 2016, cases were identified at specialty paediatric surgery centres in the United Kingdom. One year after surgical repair, the outcomes were reported. Five (6.1%) babies had repeat surgery for CDO-related reasons, and 23 (23%) encountered at least one central venous catheter-related problem within a year. Overall mortality before or within one year after surgical repair was 8.4 percent (95 percent CI 2.5 percent–14.4 percent), with no fatalities attributed to CDO.

One-year results for CDO are generally quite excellent, with poor outcomes primarily due to comorbidities. These statistics are valuable for national benchmarking and parental counselling.