Congenital pulmonary airway malformation (CPAM) is a rare developmental hamartomatous abnormality characterised by aberrant branching of immature bronchioles and lung replacement by cysts/disorganized tissue. CPAMs are often lobar or sublobar in nature, and 90% of lesions are discovered within the first two years of life. The incidence of CPAM covering a complete lung with a delayed adulthood presentation is exceedingly unusual; just four such cases have previously been documented.
The study describes the case of a 20-year-old lady who was diagnosed with unilateral whole lung CPAM based on radiologic evidence and had it surgically removed using video-assisted thoracoscopic surgery.
